Porphobilinogen Deaminase (HMBS) Antibody
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Catalogue No: abx001474
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US$348.00
(Size: 60 µl)
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Datasheet SDS
HMBS Antibody is a Rabbit Polyclonal antibody against HMBS. This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008].
Research Articles on Porphobilinogen Deaminase (HMBS)
| Target | Porphobilinogen Deaminase (HMBS) |
| Research Area | Metabolism |
| Clonality | Polyclonal |
| Reactivity | Human, Mouse |
| Tested Applications | WB |
| Host | Rabbit |
| Recommended dilutions | WB: 1/500 - 1/2000. Optimal dilutions/concentrations should be determined by the end user. |
| Conjugation | Unconjugated |
| Immunogen | Recombinant fusion protein corresponding to human HMBS |
| Isotype | IgG |
| Form | Liquid |
| Purification | Purified by affinity chromatography. |
| Storage | Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles. |
| Shelf Life | 12 months. |
| UniProt Primary AC | P08397 (UniProt, ExPASy) |
| UniProt Secondary AC | A8K2L0, G3V1P4, G5EA58, P08396, Q16012 |
| UniProt Entry Name | HEM3_HUMAN |
| Gene Symbol | HMBS |
| GeneID | 3145 |
| NCBI Accession | NP_000181.2 |
| KEGG | hsa:3145 |
| String | 9606.ENSP00000278715 |
| Molecular Weight | Calculated MW: 33 kDa/34 kDa/37 kDa/39 kDa Observed MW: 45 kDa |
| Buffer | PBS, pH 7.3, containing 0.02% sodium azide, 50% glycerol. |
| Concentration | 1 mg/ml |
| Availability | Shipped within 5-10 working days. |
| Note | THIS PRODUCT IS FOR RESEARCH USE ONLY. NOT FOR USE IN DIAGNOSTIC, THERAPEUTIC OR COSMETIC PROCEDURES. NOT FOR HUMAN OR ANIMAL CONSUMPTION. |
